Kidney transplantation in a patient with familial mediterranean fever complicated by secondary amyloidosis (clinical report)
نویسندگان
چکیده
The paper presents a clinical case of successful kidney transplantation (KTx) in patient with end-stage chronic disease (ESKD) resulting from familial Mediterranean fever (FMF). Pre-transplant preparation and posttransplant management tactics are presented. authors conclude that ESKD can be effectively treated by KTx FMF against the background ongoing pathogenetic therapy autoinflammation.
منابع مشابه
Chronic familial Mediterranean fever with development of secondary amyloidosis.
A 20-year-old Turkish male presented with fever, abdominal pain, and systemic lethargy. His clinical history revealed symptoms to be self-limiting but reoccurring over the past six months. Blood and urine specimens collected indicated renal amyloidosis. A kidney CT image indicated kidney inflammation. He was diagnosed with Familial Mediterranean Fever with the development of secondary amyloidos...
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INTRODUCTION Familial Mediterranean fever is an autosomal recessive disease that predominantly affects people of the Mediterranean coast. One of the most frequent complications of the disease is amyloidosis. This clinical entity is known as secondary (also called AA) amyloidosis. CASE PRESENTATION In this report, we describe the case of a 33-year-old Turkish man with familial Mediterranean fe...
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Postoperative respiratory distress and pulmonary edema can be seen after a wide variety of serious clinical situations, or rare diseases such as familial Mediterranean fever (FMF). FMF is a multisystemic disorder characterized by recurrent bouts of fever and pain due to inflammation of the peritoneum, synovia, or pleura. We report a case with history of FMF who developed postoperative respirato...
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A 42-year-old woman presented with an intermittent fever and chest and back pain, and an abnormal chest shadow was detected. She was diagnosed with paragonimiasis caused by Paragonimus westermani. Praziquantel therapy improved the abnormal chest shadow, but did not relieve her symptoms. She was also diagnosed with familial Mediterranean fever (FMF), and colchicine therapy resolved her symptoms....
متن کاملEarly and severe amyloidosis in a patient with concurrent familial Mediterranean fever and pseudoxanthoma elasticum.
A young woman patient had early and extensive familial Mediterranean fever (FMF)-related amyloidosis and pseudoxanthoma elasticum (PXE). She had the novel G1042S mutation in the ATP-binding cassette subfamily C member 6 (ABCC6) gene, responsible for PXE, and the mutation M694I in MEFV, the FMF gene. Both mutations were homozygous, in agreement with consanguinity in the parents. ABCC6 deficiency...
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ژورنال
عنوان ژورنال: Vestnik Transplantologii i Iskusstvennyh Organov
سال: 2023
ISSN: ['2412-6160', '1995-1191']
DOI: https://doi.org/10.15825/1995-1191-2023-1-47-51